High Systolic Pulmonary Artery Pressure is a Red Flag in Systemic Sclerosis Patients

Author: Patricia Silva
Date Published: January-2015
Source: Lung Disease News

A recent study published in the journal Rheumatology revealed that a high systolic pulmonary artery pressure (sPAP) can elevate the mortality risk in individuals with systemic sclerosis (SSc). SSc is a rare, chronic connective tissue disease, characterized by increased fibroblast activity which results in abnormal growth of connective tissue and thickening of the skin. It is a disorder more common among women and it has two forms: limited cutaneous, which is restricted to the skin on the face, hands and feet, and diffuse cutaneous that has the risk of progressing to visceral organs such as the lungs.