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Author: P. Hassoun Date Published: December-2010 Source: Presse Med
Scleroderma is a multi system disease characterized by a severe inflammatory process and
exuberant fibrosis. Lung involvement is a frequent complication and a leading cause of
morbidity and mortality in this syndrome.Two major pulmonary syndromes are associated with
scleroderma; a pulmonary vascular disorder evolving over time in to relatively isolated
pulmonary arterial hypertension (PAH), and interstitial lung disease (ILD).
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